Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
Document Type
Article
Publication Date
5-1-2022
Abstract
We present a 14-year-old boy with Loey–Dietz syndrome with severe mitral regurgitation, pectus excavatum and scoliosis. The Haller index was 25. The heart was displaced into the left hemithorax. The right inferior pulmonary vein was very close to the sternum and vertebral body. Single-stage surgery was performed. An osseo-myo-cutaneous pedicled flap was created by sterno-manubrial junction dislocation and rib resection with bilateral internal mammary arteries supplying the flap. Cardiopulmonary bypass and mitral valve replacement was performed. The defect was bridged with three straight plates. The flap was laid on top and anchored. Early outcome at three months was good. © The Author(s) 2021.
Keywords
Adolescent, Connective tissue diseases, Funnel chest, Humans, Male, Mitral valve, Sternum, Treatment outcome, Celecoxib, Fentanyl, Paracetamol, Tramadol, Adolescent, Analgesia, Article, Bleeding, Cardiopulmonary bypass, Case report, Clinical article, Computer assisted tomography, Connective tissue disease, Echocardiography, Funnel chest, Human, Intensive care unit, Loeys dietz syndrome, Lung function, Male, Mitral valve regurgitation, Mitral valve replacement, Myocutaneous flap, Noninvasive ventilation, Operation duration, Osteotomy, Outcome assessment, Pedicled skin flap, Preoperative period, Respiratory failure, Single stage open repair, Skin incision, Thorax wall reconstruction, Complication, Connective tissue disease, Diagnostic imaging, Mitral valve, Sternum, Treatment outcome
Divisions
surgerydept
Funders
None
Publication Title
Asian Cardiovascular and Thoracic Annals
Volume
30
Issue
4
Publisher
SAGE Publications Inc.