Cholecysto-appendicostomy as partial internal biliary drainage in Progressive Familial Intrahepatic Cholestasis Type 1: A case report and review of literature
Document Type
Article
Publication Date
1-1-2016
Abstract
Intractable pruritus secondary to bile salts retention in Progressive Familial Intrahepatic Cholestasis (PFIC) can be relieved surgically by diverting bile drainage from ileum to reduce bile salts reabsorption into entero-hepatic circulation. We are reporting on the successful biliary diversion in a child with PFIC, with the use of the appendix as a conduit to drain bile from gallbladder to the colon (cholecysto-appendicostomy).
Keywords
Biliary diversion, Cholecysto-appendicostomy, Intractable pruritus, Liver transplant, Progressive familial intrahepatic cholestasis
Divisions
fac_med
Publication Title
Journal of Pediatric Surgery Case Reports
Volume
4
Publisher
Elsevier
COinS