A man with concomitant polycythaemia vera and chronic myeloid leukemia: the dynamics of the two disorders
Document Type
Article
Publication Date
1-1-2010
Abstract
The co-occurrence of JAK2 V617F mutation with BCR-ABL reciprocal translocation is uncommon. We report a 60-year-old man who initially presented with phenotype of polycythemia vera (PV), which evolved into chronic myeloid leukemia and back to PV once treatment with imatinib was commenced. JAK2 V617F mutation and BCR-ABL fusion transcripts were detected in the initial sample. However, JAK2 V617F alleles diminished when BCR-ABL mRNA burden increased and reappeared once the patient was commenced on imatinib. The dynamic interaction between JAK2 V617F and BCR-ABL implies that two independent clones exist with the JAK2 V617F clone only achieving clonal dominance when BCR-ABL positive clones are suppressed by imatinib.
Keywords
Chronic myeloid leukemia, Polycythemia vera, Bcr-Abl, JAK2 V617F mutation, Stem cell
Divisions
fac_med
Publication Title
International Journal of Hematology
Volume
91
Issue
1
Publisher
Springer Verlag (Germany)