Document Type
Article (Restricted)
Publication Date
1-1-2004
Abstract
Familial hemophagocytic lymphohistiocytosis is a disorder which presents with fever, pancytopenia, liver dysfunction and also an increase in non-malignant histiocytes with prominent hemophagocytosis in various organs. It is usually difficult to distinguish from other hemophagocytic syndrome in the absence of family history. It rarely manifests in adults. Chemotherapy is usually indicated. Here, we report the occurrence of this disorder in two brothers in their twenties.
Keywords
Familial hemophagocytic lymphohistiocytosis, hemophagocytic syndrome
Divisions
fac_med
Publication Title
Medical Journal of Malaysia
Volume
59
Issue
1
Publisher
Malaysian Medical Association
Additional Information
DH
COinS